Acquired hemophilia A in a case of purple urine bag syndrome

Submitted: 5 March 2024
Accepted: 19 April 2024
Published: 16 May 2024
Abstract Views: 160
PDF: 99
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The rare hemorrhagic disorder known as acquired hemophilia A (AHA) is brought on by the spontaneous development of autoantibodies against coagulation factor VIII (FVIII). It may be secondary to autoimmune diseases or cancers, or it may be idiopathic. Less than 10% of cases may have an infection as a secondary cause. We present the case of a 90-year-old anemic woman who was admitted to the hospital. She contracted a urinary tract infection (UTI) while in the hospital, and her urine took on a distinct purple hue. She had poor hemorrhagic manifestations and a prolonged partial thromboplastin time. After ruling out autoimmune and neoplastic causes, we diagnosed AHA as a result of a UTI caused by Enterococcus faecalis.



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How to Cite

Gammaldi, V., Guida, A., Bologna, C., De Sena, A., Lugarà, M., De Luca, C., Granato Corigliano, F., Guerra, M., Oliva, G., Mocerino, L., Zarrella, A. F., Coppola, M. G., Nuzzo, V., Tirelli, P., & Madonna, P. (2024). Acquired hemophilia A in a case of purple urine bag syndrome. Italian Journal of Medicine, 18(2).