https://doi.org/10.4081/itjm.2023.1595
Adult-onset Still’s disease with secondary macrophage activation syndrome: a case report
Published: 29 May 2023
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
We describe a case of adult-onset Still’s disease (AOSD) with secondary macrophage activation syndrome. AOSD is a rare disease with unknown origin. Rarely it’s complicated by secondary macrophage activation syndrome, which is a life-threatening disorder. Because the diagnosis of AOSD is essential for exclusion and complications are life-threatening, it is mandatory for a prompt and extensive diagnostic workup and treatment.
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How to Cite
Nicoletti, G., Bonelli, A., Clemente, R., Ciuffreda, S., Dentamaro, G., La Masa, A. T., Lascaro, V., & Santarcangelo, P. (2023). Adult-onset Still’s disease with secondary macrophage activation syndrome: a case report. Italian Journal of Medicine, 17(1). https://doi.org/10.4081/itjm.2023.1595
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